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VON HIPPEL-LINDAU TUMOR SUPPRESSOR PROTEIN
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DeCS
Descriptor
English
:
Von Hippel-Lindau Tumor Suppressor Protein
Descriptor
Spanish
:
Proteína Supresora de Tumores del Síndrome de Von Hippel-Lindau
Descriptor
Portuguese
:
Proteína Supressora de Tumor Von Hippel-Lindau
Tree Number:
D08.811.464.938.750.875
D12.776.624.776.865
Definition
English
:
A ubiquitin-protein ligase that mediates OXYGEN-dependent polyubiquitination of
HYPOXIA-INDUCIBLE FACTOR 1
, ALPHA SUBUNIT. It is inactivated in VON HIPPEL-LINDAU
SYNDROME.
Entry Combination - descr/qualif
English
:
Von Hippel-Lindau Tumor Suppressor Protein
/
deficiency
use
von Hippel-Lindau Disease
History Note
English
:
2006(1995)
Allowable Qualifiers
English
:
AD
administration & dosage
AE
adverse effects
AN
analysis
AI
antagonists & inhibitors
BI
biosynthesis
BL
blood
CF
cerebrospinal fluid
CS
chemical synthesis
CH
chemistry
CL
classification
CT
contraindications
DU
diagnostic use
DE
drug effects
EC
economics
GE
genetics
HI
history
IM
immunology
IP
isolation & purification
ME
metabolism
PK
pharmacokinetics
PD
pharmacology
PH
physiology
PO
poisoning
RE
radiation effects
SE
secretion
ST
standards
SD
supply & distribution
TU
therapeutic use
TO
toxicity
UL
ultrastructure
UR
urine
Record Number:
50588
Unique Identifier:
D051794
Occurrence in VHL
:
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DeCS
CID-10
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